结缔组织增生性小圆细胞肿瘤 - 诊断与治疗 - 妙佑医疗国际

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结缔组织增生性小圆细胞肿瘤

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诊断

结缔组织增生性小圆细胞肿瘤可通过检测细胞样本进行诊断。这种癌症发生于软组织中形成异常细胞时。它通常发生在腹部内衬的组织中。为了获取这些细胞，可能需要手术，或能够穿过皮肤的一根针。这些细胞将被送往实验室进行检测。可能还需要进行影像学检查，例如超声检查、CT 扫描、MRI 和 PET。

Our caring team of Mayo Clinic experts can help you with your 结缔组织增生性小圆细胞肿瘤-related health concerns

治疗

外科手术通常用于治疗结缔组织增生性小圆细胞肿瘤。这种癌症发生在软组织中有异常细胞形成时。它通常发生在腹部内衬的组织中。外科医生会努力消除癌症。其他的治疗方法可能包括用强力药物进行化疗和用强能量束进行放射治疗。

Surgery

The goal of surgery is to remove all of the cancer. It might not be possible if the cancer has grown into nearby organs. If that happens, your health care provider may recommend chemotherapy with powerful drugs to shrink the cancer first. When it's not possible to remove the cancer entirely, your surgeon may work to remove as much as possible. Chemotherapy and radiation may be recommended after surgery to kill any cancer cells that might remain.

Chemotherapy

Chemotherapy uses powerful drugs to kill cancer cells. Chemotherapy may be used before surgery to shrink the cancer. This makes it easier to remove with surgery. Chemotherapy may also be used after surgery to kill any cells that might remain after the operation. Chemotherapy might also be an option for cancer that spreads to other parts of the body. In this situation, chemotherapy may help control symptoms, such as pain. Chemotherapy options might include: Chemotherapy that affects the whole body. Chemotherapy is most often given as a drug that's injected through a vein. The medicine travels throughout your body. The medicine kills quickly growing cells, including cancer cells. It can be used to treat desmoplastic small round cell tumors anywhere in the body. Chemotherapy given only to the abdomen. For desmoplastic small round cell tumors in the abdomen, chemotherapy drugs can be given directly to the area around your abdominal organs. This part of the body is called the peritoneal cavity. To give chemotherapy to this area only, the drugs are heated and infused into the abdomen. The drugs are left in place for a set period of time and then removed. This procedure is called hyperthermic intraperitoneal chemotherapy (HIPEC). It might be an option after surgery.

Radiation therapy

Radiation therapy uses powerful beams of energy to kill cancer cells. The energy can come from sources such as X-rays and protons. During radiation therapy, you lie very still on a table and a machine moves around you. The machine directs radiation to precise points on your body. For desmoplastic small round cell tumors that affect the abdomen, radiation might be an option to kill cancer cells that remain after surgery. If your cancer has spread to other areas of the body, radiation might be an option to help control signs and symptoms, such as pain.

Targeted drug therapy

Targeted drug treatments attack specific chemicals present within cancer cells. By blocking these chemicals, targeted drug treatments can cause cancer cells to die. Targeted therapy might be recommended if your cancer comes back after treatment. It may also be offered if your cancer has spread to other parts of the body. Your health care provider may have your cancer cells tested to see if targeted therapy drugs are likely to work against your cancer. Targeted therapy can be used alone or combined with chemotherapy. 申请 Mayo Clinic 预约

妥善处理与支持

Being diagnosed with cancer can feel overwhelming. With time you'll find ways to cope with the distress and uncertainty of cancer. Until then, you may find it helps to: Learn enough about cancer to make decisions about your care. Ask your health care provider for details about your cancer. Ask about your treatment options. If you like, ask about your prognosis. As you learn more about desmoplastic small round cell tumors, you may become more confident in making treatment decisions. Keep friends and family close. Keep your close relationships strong. They will help you deal with your diagnosis and the impact it has on your life. Friends and family can provide the practical support you'll need. For example, they can help with tasks like taking care of your home if you're in the hospital. They can serve as emotional support when you feel overwhelmed by cancer. Find someone to talk with. Find a good listener who is willing to listen to you talk about your hopes and fears. This may be a friend or family member. The concern and understanding of a counselor, medical social worker, clergy member or cancer support group also may be helpful. Ask your provider about support groups in your area. Or check with a cancer organization, such as the National Cancer Institute or the American Cancer Society.

准备您的预约

If your health care provider suspects you have a desmoplastic small round cell tumor, you may be referred to a specialist. Often this is a doctor who specializes in treating cancer. This doctor is called an oncologist. Because appointments can be brief, and there's often a lot to discuss, it's a good idea to arrive prepared. Here's some information to help you get ready.

What you can do

Write down any symptoms you're experiencing, including any that may seem unrelated to the reason for which you scheduled the appointment. Make a list of all medications, vitamins or supplements that you're taking. Ask a family member or friend to come with you. Sometimes it can be difficult to remember all the information provided to you during an appointment. Someone who accompanies you may remember something that you missed or forgot. Write down questions to ask your health care provider. Your time with your provider is limited. Prepare a list of questions to help you make the most of your time together. List your questions from most important to least important in case time runs out. For desmoplastic small round cell tumors, some basic questions to ask include: Do I have cancer? Are there other possible causes for my symptoms? What kinds of tests do I need to confirm the diagnosis? Do these tests require any special preparation? What stage is the cancer? What treatments are available for desmoplastic small round cell tumors, and which do you recommend? Can the cancer be removed? What types of side effects can I expect from treatment? Are there any alternatives to the primary approach that you're suggesting? I have other health conditions. How can I best manage these conditions together? Are there any dietary or activity restrictions that I need to follow? What's my prognosis? Are there any brochures or other printed material that I can take with me? What websites do you recommend? Should I get additional treatments before or after an operation? Is the surgeon you're recommending experienced in this specific type of cancer operation?

What to expect from your doctor

Your provider is likely to ask you a number of questions, such as: When did you first notice your signs and symptoms? Are you experiencing pain? Does anything seem to improve your symptoms? What, if anything, appears to worsen your symptoms? In addition to the questions that you've prepared, don't hesitate to ask other questions. 来自妙佑医疗国际员工在 Mayo Clinic 治疗申请 Mayo Clinic 预约症状与病因医生与科室 June 01, 2022 打印 Share on: FacebookTwitterWeChat

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What's the difference between proton vs traditional radiation? 21 Replies Sat, Feb 12, 2022 chevron-right Starting Proton Treatments for Prostate Cancer: Any experiences? 12 Replies Sat, Feb 05, 2022 chevron-right What's your experience: proton SBRT non small cell lung cancer? 5 Replies Thu, Sep 23, 2021 chevron-right See more discussions 显示参考文献 Goldblum JR, et al. Other malignant soft tissue tumors, including those of uncertain type. In: Enzinger and Weiss's Soft Tissue Tumors. 7th ed. Elsevier; 2020. https://www.clinicalkey.com. Accessed April 29, 2022. Al-Ibraheemi A, et al. Desmoplastic small round cell tumors with atypical presentations: A report of 34 cases. International Journal of Surgical Pathology. 2019; doi:10.1177/10668969188171. Mora J, et al. Desmoplastic small round cell tumor 20 years after its discovery. Future Oncology. 2015; doi:10.2217/FON.15.32. Desmoplastic small round cell tumors (DSRCT). National Cancer Institute. https://www.cancer.gov/pediatric-adult-rare-tumor/rare-tumors/rare-soft-tissue-tumors/desmoplastic-small-round-cell-tumors. Accessed April 29, 2022. Subbiah V, et al. Multimodality treatment of desmoplastic small round cell tumor: Chemotherapy and complete cytoreducetive surgery improve patient survival. Clinical Cancer Research. 2018; doi:10.1158/1078-0432.CCR-18-0202. Chicago Consensus Working Group. The Chicago consensus of peritoneal surface malignancies: Management of desmoplastic small round cell tumor, breast and gastrointestinal stromal tumors. Cancer. 2020; doi:10.1002/cncr.32856.